Dr.Payal Mukherji

Dr.NEHA SHILPY, Dr. Suchitra Kumari, dr. SINHA VIDYA BHUSHAN

Abstract

Abstract- Straatsma Syndrome is a rare condition which presents as significant vision loss associated with triad of amblyopia, myopia and myelinated nerve fibres in retina, sometimes associated with strabismus. In this case report, we document a case of reverse Straatsma Syndrome exhibiting unilateral hypermetropia, amblyopia and myelinated nerve fibres in retina.

Objective- Ophthalmologic signs and symptoms were evaluated in a patient diagnosed with reverse Straatsma syndrome.

Materials and Methods- A 22 years old male presented with unilateral diminution of vision of left eye (LE) since childhood. Complete ophthalmologic examination showed anisometropic hypermetropic ambylopia of +8DS/ +3.5DC x 90◦ in left eye (LE), correctable to 6/60 and myelinated nerve fibres in left eye retina superior to optic disc. The right eye (RE) after refractive correction of +1.5 DS showed 6/6 vision.

Result- Patient was given full refractive correction of RE and counseled for the condition in LE.