DR. NAMITHA PRAKASH

Dr.Rekha B.K. Mudhol

Abstract

VKH disease is a multisystem autoimmune inflammatory disorder with ocular,auditory,skin,neurologic involvement.

Objective-To report a case of 46yr old female who was referred from neurology with C/O headache and diminution of vision in both eyes since 15 days,with no history of trauma/eye surgery / previous ocular disease.On examination,VA:BE:CF1 mtr.Anterior segment:AC cells+ in BE.IOP(mmHg)-OD:7.8,OS:8.2by NCT.Posterior segment:BE-Hyperemic oedematous disc,punctate choroidal infiltration with areas of exudative retinal detachment.B scan revealed choroidal thickening,MRI confirmed it.FFA-BE:Punctate hyperfluorescence over the posterior pole with leakage and staining of disc.Serological testing for infectious pathologies and ANA profile was negative.CSFanalysis:inconclusive.She was started on IV steroids along with steroid eye drops.Later,switched to oral steroids along with immunosuppressants.Patient responded well to the above treatment.VA improved with regression of symptoms& signs