DR. MANOJ SHETTIGAR

Dr.Satvir Singh, Dr.Monika Dahiya, Dr.Aakash Sharma

Abstract

55 years old male presented with diminution of vision in both eye for the last 3 years which was not associated with any pain, redness and photophobia. BCVA was 6/60 in both eyes. Anterior Segment examination showed both eye NO3 NC3 (LOCS III). Fundus examination showed tiny shiny intraretinal crystals overlying a circular region of RPE atrophy centered on the fovea with peripapillary sparing of RPE and no typical flecks seen in both eyes and left eye fundus showing atrophic RPE patch surrounding hyperpigmented area. OCT showed severe foveal thinning with atrophy of overlying retina with rarified Ellipsoid zone in both eyes .Central Macular thickness (CMT) of right eye was 128um and left eye was 141um with subfoveal hyperreflective foci. Stargardt disease clinical spectrum varies widely. Early onset of disease is associated with more aggressive disease course. Cases of late onset disease (i.e., after 4th decade) are quite rare. There is no approved treatment for Stargardt dystrophy.