Dr.SUNEEL KUMAR

Dr. ABHIDNYA SURVE, Dr.Shorya Vardhan Azad, Dr.AKSHAYA BALAJI

Abstract

Bietti crystalline dystrophy, a rare autosomal recessive hereditary disorder, It is characterised by crystalline deposits and hence called as crystalline retinopathy. The retinopathy progresses with age showing decrease in the number of crystalline deposits and increase in the area of chorioretinal degeneration which spread in a centrifugal pattern. Thus, BCD can be confused with other disorders with crystalline-like deposits and chorioretinal degenerations. Here, we discuss BCD and the role of various imaging techniques using different platforms (FFA, FAF, OCT near-infrared reflectance, red-free) with special emphasis on the NIR-R and RF imaging in BCD.

Our report emphasizes, the superiority of IR reflectance and RF imaging compared to color fundus photography, FAF and retinal (green/red) reflectance in demonstrating retinal crystals in patients of BCD, facilitating early diagnosis, monitoring and follow-up in these cases.